Cic edizioni internazionali
Oral Implantology

NEW MEDICAL AND SURGICAL FINDINGS IN MULTIDISCIPLINARY APPROACH OF GORLIN-GOLTZ SYNDROME

Original research, 121 - 128
doi: 10.11138/orl/2018.11.2.121
Tag this article
Abstract
Full text PDF
Objectives. Gorlin-Goltz syndrome (GGS) is a rare autosomal dominant disorder. The disease shows multiple organ involvement with variable clinical presentation. A multidisciplinary approach is required for its prompt clinical diagnosis and management. The diagnosis of the syndrome was based on its clinical presentation, radiological features and histopathological findings.
Methods. This paper highlights a surgical and medical treatment of a case of GGS. A 42-years-old Italian female, affected by GGS, was referred to our surgical department for evaluation of multiple naevoid basal cell epithelioma and recurrent radiolucent jaw lesions. The syndrome was diagnosed based on its clinical presentation, radiological features and histopathological findings.
Results. Removal of basal cell carcinomas and enucleation of the jaw cysts along with chemical cauterization with Carnoy's solution were performed under general anesthesia. In the left side a mandibular resection BRC according to Urken classification
was necessary, and a free fibula flap through a minimally invasive technique was harvested for mandibular reconstruction.
During follow-up no sign of recurrence was detected, ongoing implant oral rehabilitation.
Conclusion. Gorlin-Goltz syndrome (GGS) is a rare disorder. As we describe on the paper the disease shows multiple organ involvement with variable clinical presentation. We suggest a multidisciplinary approach for its prompt clinical diagnosis and management.

Vol. XI (No. 3) 2018 July-September

  1. LED LIGHT, MUSIC BINAURAL, AROMATHERAPY AND STRESS
    Mandrillo P.M., Fischetto G., Candotto V., Palmieri A., Avantaggiato A., Lauritano D., Carinci F.
  2. COMPARATIVE CLINICAL STUDY BETWEEN ZIRCONIUM-CERAMIC AND METAL-CERAMIC FIXED REHABILITATIONS
    Corsalini M., Di Venere D., Carossa M., Ripa M., Sportelli P., Cantatore F., De Rinaldis C., Di Santantonio G., Lenoci G., Barile G., Rapone B.
  3. EVALUATION OF IDIOPATHIC SCOLIOSIS PATIENTS IN TERMS OF TEMPOROMANDIBULAR JOINT DISORDERS: A PILOT STUDY
    Benli M., Gargari M., Gokcen-Rohling B., Akgul T., Evlioglu G., Ceruso F.M.
  4. IMPACT OF A RIGID ORAL HYGIENE MAINTENANCE PROGRAM ON PERI-IMPLANT TISSUE HEALTH: RETROSPECTIVE ANALYSIS OF A 3-YEAR CLINICAL AND RADIOLOGICAL FOLLOW-UP OF IMPLANTS SUPPORTING ALL-ON-4 FULL-ARCH RESTORATIONS
    Todisco M., Gargari M.
  5. CONVENTIONAL IMPRESSION VS INTRAORAL SCANNER FOR CAD/CAM PARTIAL RESTORATIONS
    Campanella V., Libonati A., Angotti V., Resci T., Di Taranto V., Mea A., Giuca G., Gallusi G.
  6. THE EFFECT OF DIFFERENT POLISHING SYSTEMS ON THE SURFACE ROUGHNESS OF TWO RESTORATIVE DENTAL MATERIALS
    Libonati A., Gallusi G., Angotti V., Di Taranto V., Mea A., Casella S., Campanella V.
Last Viewed articles: la lista degli ultimi x visitati.
  1. NEW MEDICAL AND SURGICAL FINDINGS IN MULTIDISCIPLINARY APPROACH OF GORLIN-GOLTZ SYNDROME
    Russillo A., Beltramini G.A., Romano M., Baserga C., Bolzoni A.R., Rossi D.S.
    doi: 10.11138/orl/2018.11.2.121
credits