Cic edizioni internazionali
Oral Implantology

NEW MEDICAL AND SURGICAL FINDINGS IN MULTIDISCIPLINARY APPROACH OF GORLIN-GOLTZ SYNDROME

Original research, 121 - 128
doi: 10.11138/orl/2018.11.2.121
Tag this article
Abstract
Full text PDF
Objectives. Gorlin-Goltz syndrome (GGS) is a rare autosomal dominant disorder. The disease shows multiple organ involvement with variable clinical presentation. A multidisciplinary approach is required for its prompt clinical diagnosis and management. The diagnosis of the syndrome was based on its clinical presentation, radiological features and histopathological findings.
Methods. This paper highlights a surgical and medical treatment of a case of GGS. A 42-years-old Italian female, affected by GGS, was referred to our surgical department for evaluation of multiple naevoid basal cell epithelioma and recurrent radiolucent jaw lesions. The syndrome was diagnosed based on its clinical presentation, radiological features and histopathological findings.
Results. Removal of basal cell carcinomas and enucleation of the jaw cysts along with chemical cauterization with Carnoy's solution were performed under general anesthesia. In the left side a mandibular resection BRC according to Urken classification
was necessary, and a free fibula flap through a minimally invasive technique was harvested for mandibular reconstruction.
During follow-up no sign of recurrence was detected, ongoing implant oral rehabilitation.
Conclusion. Gorlin-Goltz syndrome (GGS) is a rare disorder. As we describe on the paper the disease shows multiple organ involvement with variable clinical presentation. We suggest a multidisciplinary approach for its prompt clinical diagnosis and management.

Vol. XI (No. 4) 2018 October-December

  1. CLINICAL EFFECTS OF LACTOBACILLUS REUTERI PROBIOTIC IN TREATMENT OF CHRONIC PERIODONTITIS. A RANDOMIZED, CONTROLLED TRIAL
    Costacurta M., Sicuro L., Margiotta S., Ingrasciotta I., Docimo R.
  2. BONE AUGMENTATION BY PERIOSTEUM EXTENSION USING 3-DIMENSIONAL MEMORY NICKEL-TITANIUM MESH SHEETS
    Tsutsui T., Moroi A., Yoshizawa K., Hotta A., Hiraide R., Takayama A., Tsunoda T., Saito Y., Sato M., Aikawa Y., Sakamoto H., Ueki K.
  3. DENTOSKELETAL EFFECTS OF THE BITEJUMPING APPLIANCE AND THE TWIN-BLOCK APPLIANCE IN THE TREATMENT OF SKELETAL CLASS II MALOCCLUSION: A RETROSPECTIVE CONTROLLED CLINICAL TRIAL
    Tepedino M., Cretella Lombardo E., Nota A., Tecco S., Cozza P., Pavoni C.
  4. THE ROLE OF CBCT IN THE TRACTION OF BILATERAL MAXILLARY IMPACTED CANINES WITH ADJACENT LATERAL INCISORS ROOTS RESORPTED: CASE REPORT
    Fusaroli D., Danesi C., Laganà G., Mucedero M.
  5. EVALUATION OF PROSTHETIC QUALITY AND MASTICATORY EFFICIENCY IN PATIENTS WITH TOTAL REMOVABLE PROSTHESIS: STUDY OF 12 CASES
    Corsalini M., Di Venere D., Sportelli P., Magazzino D., Ripa C., Cantatore F., Cagnetta G., De Rinaldis C., Montemurro N., De Giacomo A., Laforgia A., Rapone B.
  6. FREE FLAPS FOR HEAD-AND-NECK RECONSTRUCTION: RETROSPECTIVE ANALYSIS OF A SINGLE-CENTRE EXPERIENCE
    Beltramini G.A., Segna E., Bolzoni A.R., Rossi D.S., Cherchi A., Nuti M., Baj A.
  7. HISTOLOGIC AND HISTOMORPHOMETRIC ANALYSIS OF MAXILLARY SINUS AUGMENTATION WITH DIFFERENT BIOMATERIALS. A PILOT SPLIT-MOUTH HUMAN STUDY
    Mummolo S., Nota A., Marchetti E., Capuano S., Tecco S., Marzo G., Campanella V.
Last Viewed articles: la lista degli ultimi x visitati.
  1. NEW MEDICAL AND SURGICAL FINDINGS IN MULTIDISCIPLINARY APPROACH OF GORLIN-GOLTZ SYNDROME
    Russillo A., Beltramini G.A., Romano M., Baserga C., Bolzoni A.R., Rossi D.S.
    doi: 10.11138/orl/2018.11.2.121
credits